Angiolymphoid hyperplasia with eosinophilia (ALHE) presents as an increase in immature, primarily lymphatic vessels with plump endothelial cells lining vascular spaces, often with an associated medium-sized vessel. Surrounding the vascular component is a mixed infiltrate composed of lymphocytes that may form lymphoid follicles as well as histiocytes, plasma cells, and eosinophils. Angiolymphoid hyperplasia with eosinophilia may involve the dermis and/or subcutaneous tissue, and it often occurs in young adults, typically in the head and neck region, especially on or around the ear.