Epithelioid Sarcoma: An Unusual Presentation in the Distal Phalanx of the Toe

Epithelioid sarcoma is rare soft tissue sarcoma first described by Enzinger in 1970.

The classic variant often occurs in the deep or superficial soft tissue of the distal upper extremities of individuals between the ages of 10 and 35. Due to the tumor’s benign clinical presentation, infrequent occurrence, and histological similarities with other disease processes, diagnosing epithelioid sarcoma in its early stages has become extremely difficult.

We report a rare case of epithelioid sarcoma of the toe with bone metastasis, as well as the clinical, pathological, and radiological difficulties in correctly diagnosing epithelioid sarcoma.