Clinical Review

Diagnosis and Management of Immunoglobulin Light Chain Amyloidosis


 

The term amyloidosis refers to a fascinating group of disorders that share a common pathogenesis of extracellular deposition of amyloid material. Fundamentally, it is a disorder of the secondary structure of select proteins whereby the amyloidogenic proteins are misfolded into a β-pleated sheet configuration, resulting in the formation of insoluble extracellular amyloid fibrils. The amyloid fibrils appear as amorphous eosinophilic material when hematoxylin and eosin–stained tissue is examined under light microscope. Electron microscopy reveals remarkable similarity between the amyloid fibrils derived from different precursor proteins in that they range from 7.5 to 10 nm in diameter. This ultrastructural similarity is the underlying basis for the characteristic red-green birefringence with Congo red staining observed under polarized microscopy, the pathological hallmark of the disease.

To read the full article in PDF:

Click here

Recommended Reading

Utility of routine CT scans questioned in B-cell lymphoma surveillance
MDedge Hematology and Oncology
Idelalisib and rituximab produce responses in 97% with CLL
MDedge Hematology and Oncology
Rituximab plus chlorambucil extend event-free survival in MALT lymphoma
MDedge Hematology and Oncology
Ibrutinib shows promise for CLL del 17p
MDedge Hematology and Oncology
CD30 expression in EBV+ DLBCL confers poor prognosis
MDedge Hematology and Oncology
Pomalidomide plus low-dose dexamethasone may be new standard for MM
MDedge Hematology and Oncology
Early lenalidomide delays progression of smoldering multiple myeloma
MDedge Hematology and Oncology
Immune microenvironment linked to prognosis of follicular lymphoma
MDedge Hematology and Oncology
Post-transplant Lymphoproliferative Disorders
MDedge Hematology and Oncology
Pixantrone gaining market access in EU
MDedge Hematology and Oncology